
Ectodermosis Erosiva Pluriorificialis
📋Overview
Ectodermosis Erosiva Pluriorificialis is a legacy term historically used to describe a severe form of junctional epidermolysis bullosa (JEB), a group of rare genetic skin disorders characterized by fragile skin that blisters and erodes easily. The modern preferred term is junctional epidermolysis bullosa. This condition primarily affects the skin and mucous membranes due to defects in proteins responsible for dermo-epidermal adhesion.
Medical codes (for reference)
UMLS CUI: C0038325ICD-10-CM
L51.1
MeSH
D013262
SNOMED CT (US)
73442001
Codes are provided for reference and interoperability. They are not a diagnosis.
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